Focal Pulmonary Capillary Hemangiomatosis. Case Report

Abstract

Pulmonary Capillary Hemangiomatosis (PCH) is a rare cause of pulmonary hypertension in which patients are generally young with symptoms and signs related to pulmonary hypertension. The diagnosis is usually post mortem. It is typically a bilateral diffuse pulmonary process, but it can be focal on some occasions. Histologically, it is characterized by growth of small capillaries in the interstitium and alveolar walls, this proliferation of capillaries can invade the small pulmonary vessels and bronchi. Reports of focal PCH are scarce, we present the case of a 47 year-old woman diagnosed with focal PCH.