Eosinophilic Granulomatosis with Polyangiitis: a Case Report
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Abstract
Eosinophilic granulomatosis with polyangiitis is a rare form of anti-neutrophil cytoplasm antibody-associated vasculitis of small and medium vessels, associated with extravascular eosinophilic granulomas, peripheral eosinophilia and asthma.
The authors present a case of a 68-year-old male, with late-onset asthma, rhinosinusitis and eosinophilia. A vasculitis phase was characterized by constitutional symptoms, peripheral neuropathy and a palpable purpura. Anti-neutrophil cytoplasmic antibodies were present. After 5 years of treatment, with corticosteroids and methotrexate, relapsed occurred and the patient was admitted due to arrhythmia, pneumonitis and small pulmonary nodules - an uncommon pulmonary manifestation.
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