Giant Diffuse Esophageal Leiomyomatosis. Case Report
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Abstract
Introduction: Esophageal leiomyomatosis is a benign neoplasm with an extremely low incidence of esophageal tumors and is sometimes difficult to categorize as a neoplasm or myopathy.
Clinical case: The case of a 24-year-old girl, who consulted for progressive dysphagia of one year of evolution and a history of having discovered a “spot” on her lung ten years ago, is reported. The images show a mass that occupies the middle and lower third of the esophagus and proximal megaesophagus due to obstruction at the level of the cardia. Total esophagectomy, tubulization and gastric ascent with pyloroplasty plus lateral esophagogastric anastomosis at the cervical level were performed. The pathology confirms the histology of esophageal leiomyomatosis.
Conclusion: It is a very rare pathology with few reported cases.
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