Dextrocardia and Intrathoracic Herniation of the Liver. A Rare Entity
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Abstract
Introduction: the incidence of dextrocardia as a congenital anomaly is less than 0.01% and the combination with intrathoracic herniation of the liver resembling a benign neoplasm without a history of open or blunt thoracoabdominal trauma makes it even less frequent. Clinical case: the case of a 34-year-old female patient who consults for back pain is presented. On physical examination, heart sounds are auscultated in the right hemithorax and the chest X-ray shows dextrocardia and an image that resembles a right supradiaphragmatic mass. Triphasic CT confirms the presence of a rounded protrusion of a segment of the liver through a non-open defect of the liver right hemidiaphragm. The treatment has been conservative. Conclusion: the combination of dextrocardia accompanied by herniation of a portion of the liver through a defect in the right diaphragm is an extremely rare association and published case reports are few.
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References
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