Agenesis of the Right Pulmonary Artery: a Diagnostic Challenge in Acute Pulmonary Edema
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Introduction: Right pulmonary artery agenesis and right pulmonary hypoplasia are considered rare conditions identified in early life. Approximately five cases have been reported in adulthood, two of which presented with complications such as pulmonary hypertension and acute pulmonary edema.
Case report: We present the case of a 34-year-old woman in the immediate postpartum period with clinical presentations suggestive of acute pulmonary thromboembolism. Chest CT angiography revealed a congenital vascular malformation: agenesis of the right pulmonary artery branch, unilateral pulmonary edema, and indirect evidence of pulmonary hypertension.
Conclusion: This case highlights the importance of considering vascular malformations as a cause of unilateral acute pulmonary edema with underlying pulmonary hypertension, which carries a high risk of mortality, particularly during pregnancy and the postpartum period. Its timely identification allows for targeted management and specialized follow-up.
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